上海交通大学学报(医学版)

• 病例报告 • 上一篇    

腹膜透析并发包裹性腹膜硬化症1例报道

张贺,李振元,严豪,张敏芳,王琴,王玲,倪兆慧,钱家麒,方炜   

  1. 上海交通大学 医学院附属仁济医院肾脏科,上海市腹膜透析研究中心,上海 200127
  • 出版日期:2016-11-28 发布日期:2016-11-29
  • 通讯作者: 方炜,电子信箱:fangwei_sh@126.com。
  • 作者简介:张贺(1985-),女,住院医师,硕士生;电子信箱:zhanghe_renji@126.com。
  • 基金资助:

    国家自然科学基金(81370864,81670691);上海青年医师培养资助计划;上海市教育委员会高峰高原学科建设计划(20152211)

Peritoneal dialysis with encapsulating peritoneal sclerosis: a case report

ZHANG He, LI Zhen-yuan, YAN Hao, ZHANG Min-fang, WANG Qin, WANG Ling, NI Zhao-hui, QIAN Jia-qi, FANG Wei   

  1. Department of Nephrology, Renji Hospital, Shanghai Jiao Tong University School of Medicine, Shanghai Center for Peritoneal Dialysis Research, Shanghai 200127, China
  • Online:2016-11-28 Published:2016-11-29
  • Supported by:

    National Natural Science Foundation of China,81370864,81670691; Shanghai Young Doctor Training Program; Shanghai Municipal Education Commission—Gaofeng Clinical Medicine Grant Support,20152211

摘要:

目的 ·提高对腹膜透析相关的包裹性腹膜硬化症的认识和防治。方法 ·分析1例退出腹膜透析后发生包裹性腹膜硬化症并给予药物治疗的病例。结果 · 1例因腹膜超滤衰竭退出腹膜透析的血液透析患者出现肠梗阻症状,结合影像学结果,诊断为包裹性腹膜硬化症,给予药物治疗结合全胃肠外营养,临床症状有明显改善。结论 ·包裹性腹膜硬化症是腹透患者的严重并发症,早期诊断困难,预后差,严重影响着腹膜透析患者的生存质量。药物及手术治疗各有优缺点,应及时发现尽早治疗。

关键词: 包裹性腹膜硬化症, 腹膜透析, 肠梗阻

Abstract:

Objective · To improve awareness, prevention, and treatment of peritoneal dialysis-related encapsulating peritoneal sclerosis. Methods · A case developing encapsulating peritoneal sclerosis after discontinuing peritoneal dialysis and receiving medication treatment was analyzed. Results · A patient developed intestinal obstruction after discontinuing peritoneal dialysis due to peritoneal ultrafiltration failure. Combined with imaging examination, the diagnosis was encapsulating peritoneal sclerosis. Clinical symptoms were significantly improved after receiving medication treatment and total parenteral nutrition. Conclusion · Encapsulating peritoneal sclerosis is a serious complication in peritoneal dialysis patients. As the early diagnosis is difficult and the prognosis is poor, it significantly affects the quality of life. Both medication treatment and surgery have advantages and disadvantages. Early diagnosis and prompt treatment are necessary.

Key words: encapsulating peritoneal sclerosis, peritoneal dialysis, intestinal obstruction