JOURNAL OF SHANGHAI JIAOTONG UNIVERSITY (MEDICAL SCIENCE) ›› 2021, Vol. 41 ›› Issue (10): 1389-1393.doi: 10.3969/j.issn.1674-8115.2021.10.019

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Progress in surgical strategies of pulmonary atresia with ventricular septal defect

Zhi-ying SONG(), Jing-hao ZHENG()   

  1. Department of Cardiothoracic Surgery, Shanghai Children's Medical Center, Shanghai Jiao Tong University School of Medicine, Shanghai 200127, China
  • Online:2021-10-28 Published:2021-09-13
  • Contact: Jing-hao ZHENG;
  • Supported by:
    Projects of Shanghai Science and Technology Commission(19411963700)


Pulmonary atresia with ventricular septal defect is one of the most common complex right heart malformations. The existence of major aortopulmonary collateral arteries and the individual differences in pulmonary vascular development make the anatomical classification and surgical methods of this disease variable, and the treatment effect is not ideal. At present, there is still a lack of unified standards and procedures for treatment strategies such as unifocalization and staged surgery at home and abroad. This article reviews the progress of surgical diagnosis and treatment and surgical strategy of pulmonary atresia with ventricular septal defect.

Key words: pulmonary atresia, ventricular septal defect, major aortopulmonary collateral artery, surgical strategy

CLC Number: