Diagnosis and treatment of congenital vascular ring: prenatal and postnatal

doi:10.3969/j.issn.1674-8115.2022.11.015

Abstract

Abstract:

Congenital vascular ring (CVR) is a rare congenital vascular malformation. During aortic arch development, congenital variations in vessels may occur, some of which form vascular rings that cause compression around the airway and/or esophagus, causing a range of respiratory and gastrointestinal symptoms. In addition, CVR may be associated with a variety of chromosomal and genetic abnormalities and other intracardiac and extracardiac structural malformations. The treatment and prognosis varies from type to type according to differences in anatomic structure and degree of compression. With the standardization and popularization of prenatal screening of fetal congenital diseases, the liversification of postnatal assessment methods and application of new operation methods, the prenatal detection rate of CVR has been increased, and the postnatal evaluation has been more accurate. The postoperative prognosis of some diseases has been improved. However, the clinical cognition of CVR still remains to be improved. The lack of professional consultation on treatment and prognosis may cause excessive anxiety of gravida and families, and even unnecessary induction. The surgical indication, treatment and prognosis of each type of CVR still remain to reach a consensus. This review summarizes the anatomical characteristics, diagnostic methods, clinical manifestations, and treatment and prognosis of CVR types in order to improve and update the understanding of this disease, guide gravidae to make more reasonable decisions during pregnancy and provide reference for diagnosis, treatment and follow-up plan.

Key words: congenital vascular ring, fetal echocardiography, prenatal diagnosis, treatment, prognosis

CLC Number:

R725.4

GU Shuneng, WU Pengfei, WU Yurong. Diagnosis and treatment of congenital vascular ring: prenatal and postnatal[J]. Journal of Shanghai Jiao Tong University (Medical Science), 2022, 42(11): 1620-1626.

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