Abstract:

Intravenous leiomyomatosis with right atrium extension is a rare tumor with potential lethality, hormonal dependency and vascular extension. Surgical excision and hormonal therapy-based multi-discipline cooperation therapeutics may be the optimal therapy and helpful to improve the prognosis. One case of intravenous leiomyomatosis with right atrium extension which was diagnosed by examinations of echocardiography, chest and abdomen CT, CT angiography and pathology was reported in this paper. Tamoxifen and luteinising hormone-releasing hormone agonist were administered as endocrine therapy, and the tumor was resected through a two-stage approach. The patient underwent one-stage resection for the mass of right atrium and inferior vena cava, and the outcome was satisfactory.

Key words: intravenous leiomyomatosis, diagnosis, treatment